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Very Rare Condition (very + rare_condition)

Distribution by Scientific Domains

Medical Sciences	100%

Selected Abstracts

Congenital asplenia and group B streptococcus sepsis in the adult: case report and review of the literature

FEMS IMMUNOLOGY & MEDICAL MICROBIOLOGY, Issue 3 2008
Kumaran Thiruppathy
Abstract Asplenia is associated with an increased incidence of fatal and life-threatening sepsis caused by encapsulated pathogens. Isolated congenital asplenia is a very rare condition, with only 33 cases reported in the literature. The authors report another case of this condition complicated by overwhelming Group B streptococcus sepsis secondary to paronychia that was managed successfully. [source]

Rare living hypopharyngeal foreign body

HEAD & NECK: JOURNAL FOR THE SCIENCES & SPECIALTIES OF THE HEAD AND NECK, Issue 11 2006
Matthias Kuehnemund MD
Abstract Background. This is a case report about a rare hypopharyngeal foreign body causing dysphagia, dyspnea, and hemoptysis as well as melena: an ingested leech. The patient was in this condition for more than 1 week. Methods. The ingested leech, attached to the right piriform fossa partially obstructing the larynx, had to be removed under general anesthesia. Results. After removal, no further symptoms occurred. The leech was identified as the species Theromyzon tessulatum. Conclusions. Human infestation of a leech in the upper aerodigestive tract is a very rare condition in urban areas. The current literature is reviewed and the diagnostic approach as well as therapeutic options are discussed. © 2006 Wiley Periodicals, Inc. Head Neck, 2006 [source]

Cavernous hemangioma of the liver with giant cyst formation: Degeneration by apoptosis?

JOURNAL OF GASTROENTEROLOGY AND HEPATOLOGY, Issue 3 2001
Kazuhiro Hanazaki
Abstract Cavernous hemangioma of the liver with cyst formation is a very rare condition. A case of cavernous hemangioma of the liver with unilocular giant cyst formation undergoing surgical removal is reported. Notably, the patient also had Budd,Chiari syndrome with an obstructing lesion in the inferior vena cava. The cystic degeneration of the hemangioma implied a relationship with apoptosis. This is the first reported case of Budd,Chiari syndrome caused by advanced cystic degeneration of hepatic cavernous hemangioma. [source]

Cutaneous Crohn Disease in a Child

PEDIATRIC DERMATOLOGY, Issue 1 2006
Anna Luisa Pinna M.D.
It is a very rare condition, especially in children, and is easily misdiagnosed when characteristic gastrointestinal symptoms are absent. We report a 10-year-old Caucasian girl with a 6-month history of erythematous, firm tumescence of the left labium majus pudendi and moist vegetations circumscribing the anal ostium. Histologic analysis of skin biopsy specimens from both types of lesions showed a characteristic granulomatous noncaseating infiltrate throughout the dermis. Endoscopic examination and a colon biopsy specimen showed chronic granulomatous inflammation consistent with Crohn disease. Treatment with prednisolone 20 mg daily, metronidazole 250 mg three times daily, topical corticosteroids, and mupirocin ointment produced marked improvement of the vulvar edema, whereas the perianal lesion had a relapsing course. Early recognition of extra-intestinal manifestations of Crohn disease, which are extremely rare in children, may be difficult. Coexistence of contiguous and noncontiguous lesions, representing the very first signs of the disease, are further peculiarities in our patient. [source]