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Haemorrhagic Telangiectasia (haemorrhagic + telangiectasia)

Distribution by Scientific Domains
Medical Sciences100%

Kinds of Haemorrhagic Telangiectasia

  • hereditary haemorrhagic telangiectasia
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    Selected Abstracts

    Bosentan therapy for pulmonary arterial hypertension associated with hereditary haemorrhagic telangiectasia

    EUROPEAN JOURNAL OF CLINICAL INVESTIGATION, Issue 2006
    D. Bonderman
    Abstract Hereditary haemorrhagic telangiectasia (HHT) is a disorder of arteriovenous malformations and telangiectases. In rare cases affected individuals may develop typical pulmonary arterial hypertension (PAH). Vasodilator therapy has not been recommended because of a potential increase in arteriovenous shunt volume. This report is on two patients with severe HHT-associated PAH who were treated with bosentan, an oral endothelin ETA/ETB receptor antagonist. After 1 year, symptomatic and functional improvements were confirmed by haemodynamic evaluation demonstrating a significant decrease of mean pulmonary artery pressures and an increase in cardiac index, without evidence for an increase in effective shunt volume. [source]

    The diagnostic quandary of hereditary haemorrhagic telangiectasia vs.

    BRITISH JOURNAL OF DERMATOLOGY, Issue 4 2001
    CREST syndrome
    The distribution and clinical appearance of the telangiectasia in the CREST syndrome (calcinosis, Raynaud's phenomenon, oesophageal involvement, sclerodactyly, telangiectasia) and hereditary haemorrhagic telangiectasia (HHT) are very similar. Several previously reported cases of the CREST syndrome simulating HHT illustrate this diagnostic quandary. We report a patient who met the diagnostic criteria for both the CREST syndrome and HHT, and discuss the distinguishing features of the two diseases, including the distinctive histopathological findings of telangiectasia in HHT. [source]

    Hereditary haemorrhagic telangiectasia involving the bone marrow and liver

    BRITISH JOURNAL OF HAEMATOLOGY, Issue 2 2009
    Jason Willis
    No abstract is available for this article. [source]

    Hereditary haemorrhagic telangiectasia associated with vitiligo, autoimmune thyroiditis, iridocyclitis and a myelodysplastic syndrome

    CLINICAL & EXPERIMENTAL DERMATOLOGY, Issue 4 2005
    A. Grapsa
    No abstract is available for this article. [source]